Size :50ul
Clone Number:
Aliases:Alpha L fucosidase I antibody; Alpha L fucoside fucohydrolase antibody; Alpha-L-fucosidase 1 antibody; Alpha-L-fucosidase I antibody; Alpha-L-fucoside fucohydrolase 1 antibody; FUCA antibody; FUCA1 antibody; FUCO_HUMAN antibody; fucosidase; alpha-L; tissue antibody; fucosidase; alpha-L- 1; tissue antibody; Tissue alpha L fucosidase antibody; Tissue alpha-L-fucosidase antibody
Product Type:Polyclonal Antibody
Immunogen Species:Homo sapiens (Human)
UniProt ID:P04066
Immunogen:Fusion protein of Human FUCA1
Raised in:Rabbit
Species Reactivity:Human, Mouse
Tested Applications:ELISA, WB, IHC; ELISA:1:2000-1:5000, WB:1:500-1:2000, IHC:1:50-1:200
Background:The protein encoded by this gene is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids. Mutations in this gene are associated with fucosidosis (FUCA1D), which is an autosomal recessive lysosomal storage disease. A pseudogene of this locus is present on chr 2.
Clonality:Polyclonal
Isotype:IgG
Purification Method:Antigen affinity purification
Conjugate:Non-conjugated
Buffer:-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
Form:Liquid
Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names:FUCA1
Research Areas:Metabolism;Signal transduction