Size :50ul
Clone Number:
Aliases:1110061O17Rik antibody; 4-1 antibody; 4-glucantransferase antibody; 6-glucosidase antibody; 9430004C13Rik antibody; 9630046L06Rik antibody; AGL antibody; AI850929 antibody; Amylo 1 6 glucosidase 4 alpha glucanotransferase antibody; Amylo-1 antibody; Amylo-alpha-1 antibody; C77197 antibody; Dextrin 6-alpha-D-glucosidase antibody; GDE antibody; GDE_HUMAN antibody; Glycogen debrancher antibody; Glycogen debranching enzyme antibody; Glycogen storage disease type III antibody; Oligo-1 antibody
Product Type:Polyclonal Antibody
Immunogen Species:Homo sapiens (Human)
UniProt ID:P35573
Immunogen:Synthetic peptide of Human AGL
Raised in:Rabbit
Species Reactivity:Human
Tested Applications:ELISA, IHC; ELISA:1:2000-1:5000, IHC:1:25-1:100
Background:This gene encodes the glycogen debrancher enzyme which is involved in glycogen degradation. This enzyme has two independent catalytic activities which occur at different sites on the protein: a 4-alpha-glucotransferase activity and a amylo-1,6-glucosidase activity. Mutations in this gene are associated with glycogen storage disease although a wide range of enzymatic and clinical variability occurs which may be due to tissue-specific alternative splicing. Alternatively spliced transcripts encoding different isoforms have been described.
Clonality:Polyclonal
Isotype:IgG
Purification Method:Antigen affinity purification
Conjugate:Non-conjugated
Buffer:-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
Form:Liquid
Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names:AGL
Research Areas:Cancer;Metabolism;Signal transduction