Size :50ul
Clone Number:
Aliases:250/210 kDa paraneoplastic pemphigus antigen antibody; DCWHKTA antibody; Desmoplakin (DPI DPII) antibody; Desmoplakin antibody; Desmoplakin I antibody; Desmoplakin II antibody; DESP_HUMAN antibody; DP antibody; DP I antibody; DP II antibody; DPI antibody; DPII antibody; DSP antibody; KPPS2 antibody; PPKS 2 antibody; PPKS2 antibody
Product Type:Polyclonal Antibody
Immunogen Species:Homo sapiens (Human)
UniProt ID:P15924
Immunogen:Synthetic peptide of Human DSP
Raised in:Rabbit
Species Reactivity:Human, Mouse
Tested Applications:ELISA, IHC; ELISA:1:2000-1:5000, IHC:1:50-1:200
Background:Desmosomes are intercellular junctions that tightly link adjacent cells. Desmoplakin is an obligate component of functional desmosomes that anchors intermediate filaments to desmosomal plaques. The N-terminus of desmoplakin is required for localization to the desmosome and interacts with the N-terminal region of plakophilin 1 and plakoglobin. The C-terminus of desmoplakin binds with intermediate filaments. In the mid-region of desmoplakin, a coiled-coiled rod domain is responsible for homodimerization. Mutations in this gene are the cause of several cardiomyopathies and keratodermas as well as the autoimmune disease paraneoplastic pemphigus.
Clonality:Polyclonal
Isotype:IgG
Purification Method:Antigen affinity purification
Conjugate:Non-conjugated
Buffer:-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
Form:Liquid
Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names:DSP
Research Areas:Signal transduction