Size :50ul
Clone Number:
Aliases:5 @aminolevulinate synthase erythroid specific antibody; 5 aminolevulinate synthase 2 antibody; 5 aminolevulinate synthase 5 aminolevulinate synthase 2 antibody; 5 aminolevulinate synthase erythroid specific mitochondrial antibody; 5 aminolevulinic acid synthase 2 antibody; 5 aminolevulinic acid synthase antibody; 5-aminolevulinate synthase antibody; 5-aminolevulinic acid synthase 2 antibody; Alas 2 antibody; ALAS antibody; ALAS E antibody; ALAS; erythroid antibody; ALAS-E antibody; Alas2 antibody; ALASE antibody; Aminolevulinate delta synthase 2 antibody; Aminolevulinic acid synthase 2; erythroid antibody; ANH1 antibody; ASB antibody; Delta ALA synthase 2 antibody; Delta ALA synthetase antibody; Delta aminolevulinate synthase 2 antibody; Delta aminolevulinate synthase antibody; Delta-ALA synthase 2 antibody; Delta-aminolevulinate synthase 2 antibody; Erythroid specific ALAS antibody; erythroid-specific antibody; FLJ93603 antibody; HEM0_HUMAN antibody; mitochondrial antibody; OTTHUMP00000023388 antibody; OTTHUMP00000023389 antibody; OTTMUSP00000020679 antibody; RP23-338A17.1 antibody; SIDBA1 antibody; XLDPP antibody; XLEPP antibody; XLSA antibody
Product Type:Polyclonal Antibody
Immunogen Species:Homo sapiens (Human)
UniProt ID:P22557
Immunogen:Fusion protein of Human ALAS2
Raised in:Rabbit
Species Reactivity:Human, Mouse, Rat
Tested Applications:ELISA, WB; ELISA:1:2000-1:5000, WB:1:500-1:2000
Background:The product of this gene specifies an erythroid-specific mitochondrially located enzyme. The encoded protein catalyzes the first step in the heme biosynthetic pathway. Defects in this gene cause X-linked pyridoxine-responsive sideroblastic anemia. Alternatively spliced transcript variants encoding different isoforms have been identified.
Clonality:Polyclonal
Isotype:IgG
Purification Method:Antigen affinity purification
Conjugate:Non-conjugated
Buffer:-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
Form:Liquid
Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names:ALAS2
Research Areas:Others