Size :100ul
Clone Number:
Aliases:Fkrp antibody; FKRP_HUMAN antibody; FLJ12576 antibody; Fukutin related protein antibody; Fukutin-related protein antibody; LGMD2I antibody; MDC1C antibody; MGC2991 antibody
Product Type:Polyclonal Antibody
Immunogen Species:Homo sapiens (Human)
UniProt ID:Q9H9S5
Immunogen:Synthesized peptide derived from N-terminal of Human FKRP.
Raised in:Rabbit
Species Reactivity:Human, Mouse, Rat
Tested Applications:ELISA, WB; WB:1:500-1:3000
Background:Could be a transferase involved in the modification of glycan moieties of alpha-dystroglycan (DAG1).
Brockington M., Am. J. Hum. Genet. 69:1198-1209(2001).
Ota T., Nat. Genet. 36:40-45(2004).
Brockington M., Hum. Mol. Genet. 10:2851-2859(2001).
Clonality:Polyclonal
Isotype:IgG
Purification Method:The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Conjugate:Non-conjugated
Buffer:Rabbit IgG in phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol.
Form:liquid
Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names:FKRP
Research Areas:Signal transduction