Size :50ug
Clone Number:
Aliases:Fkrp antibody; FKRP_HUMAN antibody; FLJ12576 antibody; Fukutin related protein antibody; Fukutin-related protein antibody; LGMD2I antibody; MDC1C antibody; MGC2991 antibody
Product Type:Polyclonal Antibody
Immunogen Species:Homo sapiens (Human)
UniProt ID:Q9H9S5
Immunogen:Recombinant Human Fukutin-related protein (28-140AA)
Raised in:Rabbit
Species Reactivity:Human
Tested Applications:
Background:Transferase involved in the biosynthesis of the phosphorylated O-mannosyl trisaccharide (N-acetylgalactosamine-beta-3-N-acetylglucosamine-beta-4-(phosphate-6-)mannose), a carbohydrate structure present in alpha-dystroglycan (DAG1), which is required for binding laminin G-like domain-containing extracellular proteins with high affinity.
Clonality:Polyclonal
Isotype:IgG
Purification Method:>95%, Protein G purified
Conjugate:FITC
Buffer:Preservative: 0.03% Proclin 300
Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
Form:Liquid
Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names:FKRP
Research Areas:Signal transduction