Size :50ul
Clone Number:
Aliases:BHD antibody; BHD skin lesion fibrofolliculoma protein antibody; Birt Hogg Dube syndrome protein antibody; Birt-Hogg-Dube syndrome protein antibody; DKFZp547A118 antibody; FLCL antibody; Flcn antibody; FLCN_HUMAN antibody; FLJ45004 antibody; FLJ99377 antibody; Folliculin antibody; MGC17998 antibody; MGC23445 antibody
Product Type:Polyclonal Antibody
Immunogen Species:Homo sapiens (Human)
UniProt ID:Q8NFG4
Immunogen:Fusion protein of Human FLCN
Raised in:Rabbit
Species Reactivity:Human, Mouse, Rat
Tested Applications:ELISA, IHC; ELISA:1:2000-1:10000, IHC:1:100-1:300
Background:This gene is located within the Smith-Magenis syndrome region on chromosome 17. Mutations in this gene are associated with Birt-Hogg-Dube syndrome, which is characterized by fibrofolliculomas, renal tumors, lung cysts, and pneumothorax. Alternative splicing of this gene results in two transcript variants encoding different isoforms.
Clonality:Polyclonal
Isotype:IgG
Purification Method:Antigen affinity purification
Conjugate:Non-conjugated
Buffer:-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
Form:Liquid
Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names:FLCN
Research Areas:Cancer